Anesthetic management of paediatric cataract surgery with Marinesco-Sjogren Syndrome

Akshay PT 1, * and Shilpashri AM 2

1 Final year Post Graduate, Department of Anaesthesia, J.J.M Medical College, Davangere, Karnataka, India. 
2 Professor, Department of Anaesthesia, J.J.M Medical College, Davangere, Karnataka, India.
 
Case Study
World Journal of Biology Pharmacy and Health Sciences, 2024, 20(01), 214–215.
Article DOI: 10.30574/wjbphs.2024.20.1.0733
Publication history: 
Received on 28 August 2024; revised on 05 October 2024; accepted on 07 October 2024
 
Abstract: 
Marinesco-Sjogren syndrome (MSS) is a rare autosomal recessive disorder characterized by cataracts, muscle weakness, mental retardation, and cerebellar ataxia. Patients with MSS may be posted for surgery early in the age for cataract aspiration, which requires unique anesthetic considerations involving myopathy, hypotonicity, growth and mental retardation.
 
Keywords: 
Marinesco-Sjogren syndrome (MSS); Cataract; Paediatric; Myopathy; Respiratory Depression; Ataxia. 
 
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Copyright information: 
Copyright © 2024 Author(s) retain the copyright of this article. This article is published under the terms of the Creative Commons Attribution Liscense 4.0