Double outlet right ventricle accompanied by complex congenital anomalies: A rare association

Akhil Mehrotra *, Faiz Illahi Siddiqui and Mohammad Shaban

Prakash Heart Station, Nirala Nagar, Lucknow, UP, India, 226020.
 
Research Article
World Journal of Biology Pharmacy and Health Sciences, 2024, 18(03), 199–215
Article DOI: 10.30574/wjbphs.2024.18.3.0332
Publication history: 
Received on 26 April 2024; revised on 10 June 2024; accepted on 13 June 2024
 
Abstract: 
Double outlet right ventricle (DORV) comprises a heterogeneous series of associated cardiac anomalies that involve the RV outflow tract in which both of the great arteries arise entirely or predominantly from the RV. The anatomic dysmorphology is variable, and there may be associated cardiac anomalies.
We report here a case of a complex cyanotic heart disease in a 14 year old adolescent comprising of DORV accompanied by multiple congenital cardiac anomalies: single atrium, complete AV canal defect, severe AV valve regurgitation, D-malposition of great arteries, subaortic obstruction and pulmonary valvular stenosis.
 
Keywords: 
DORV; Single atrium; Remote VSD; Atrioventricular septal defect; Pulmonary stenosis; Subaortic stenosis; Subaortic membrane; Subpulmonic conus
 
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