Pediatric factor X111 deficiency with retroperitoneal hematoma: An anaesthesiologist’s challenge

A 12 year old girl, known case of factor X111 deficiency came with complains of pain abdomen and fever was diagnosed with retroperitoneal hematoma. Patient was on regular cryoprecipitate and FFP transfusions since childhood for factor deficiency. Initial blood investigations shows anemia and deranged coagulation profile. Ultrasonography shows retroperitoneal hematoma. Patient posted for surgical exploration. After pre operative evaluation and optimisation by blood products transfusion. Surgery was done under general anaesthesia with blood products reserved for emergency management of intra operative bleeding. Intra op was uneventful. Postoperatively there were no complications.