National Reference Center for Neonatology, Children's Hospital Chu Rabat, Research team in health and nutrition of the mother-child couple. Faculty of Medicine and Pharmacy. Mohamed V University Rabat, Morocco.
Received on 08 March 2023; revised on 17 April 2023; accepted on 19 April 2023
Congenital portosystemic fistula (CPF) is a congenital malformation defined by one or more communications between a hepatic portal venous system and a systemic venous cava. Other terminologies exist in the literature, in particular for extrahepatic communications, such as "Abernethy malformation". It may be associated with other malformations or syndromes. Because of this non-physiological vascular communication, PFC can lead to the development of extrahepatic complications: hepatic encephalopathy and pulmonary vascular diseases (hepato-pulmonary syndrome or pulmonary hypertension). It can also lead to hepatic complications with the appearance of benign or malignant tumors and biological and metabolic disorders.
We report the case of a newborn with a portosystemic hepatic fistula discovered during neonatal jaundice with cutaneous angiomatosis.
Fistula; Congenital; Portosystemic; Abernethy; Neonatal; Hepatic
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I Elouardighi, I Zizi, L El Iaziji, N Amalik and A Barkat. Congenital Portosystemic Hepatic Fistula: A case report. World Journal of Biology Pharmacy and Health Sciences, 2023, 14(01), 145–149. Article DOI: https://doi.org/10.30574/wjbphs.2023.14.1.0188